A Rare Case of Rathke Cleft Cyst with Xanthogranulomatous Change |
라스케열낭종의 황색육아종성 변화 1례 |
김일만 |
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Abstract |
A rare case of symptomatic Rathke cleft cyst (RCC) with xanthogranulomatous change is
reported; which is discovered in a 16-year-old girl presenting with primary amenorrhea and no
development of secondary sexual characteristics. The endocrinological assessment revealed the
patient had a hypogonadotropic hypogonadism. Brain magnetic resonance imaging demonstrated a
17 mm sized cystic lesion with rim enhancement in the intra- and suprasellar region. Via an
endonasal microscopic approach; the cyst was completely decompressed and the cyst wall was
partly excised. The cyst contents were confirmed intraoperatively with distinct colors and
consistencies. Pathological examination of surgical specimen showed a nonciliated columnar
epithelial lesion associated with xanthogranulomatous changes. The author speculate that
xanthogranulomas in the sellar region might be caused by reaction to the presence of RCC. |
Key Words:
Amenorrhea,
Hypogonadism, Rathke cleft cyst |
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