CT Findings of 
Diffuse Pulmonary Lymphangiomatosis : A case report

Keimyung Medical Journal 1996;15(3):269-273.

CT Findings of Diffuse Pulmonary Lymphangiomatosis : A case report

미만성 폐 림프관종증의 CT 소견 : 증례보고

이진희; 서수지; 우성구; 이희정; 권건영

Abstract

Diffuse pulmonary lymphangiomatosis(DPL) is a very rare; progressive pulmonary abnormality of lymphatic system that occurs in children and young adults. We presented CT findings of DPL in a young girl; which was characterized by diffuse; smooth thickening of bronchovascular bundles and interlobular septa especiallly in the subpleural regions of both lower lobes; associated with recurrent pleural effusion. Pathologically; the disorder revealed increased numbers of anastomosing lymphatic channels in the pleura and subpleural interlobular septa.

Key Words: Diffuse pulmonary lymphangiomatosis, lymphatic system